Cutaneous polyarteritis nodosa: a comprehensive review
Identifieur interne : 001730 ( Main/Exploration ); précédent : 001729; suivant : 001731Cutaneous polyarteritis nodosa: a comprehensive review
Auteurs : Aaron Joseph Morgan [États-Unis] ; Robert A. Schwartz [États-Unis]Source :
- International Journal of Dermatology [ 0011-9059 ] ; 2010-07.
English descriptors
- Teeft :
- Acad, Acad dermatol, Arch dermatol, Arthralgia, Arthritis rheum, Case report, Clinical course, Complement levels, Constitutional symptoms, Corticosteroid, Cpan, Cutaneous, Cutaneous periarteritis nodosa, Cutaneous polyarteritis nodosa, Cutaneous vasculitis, Dermatol, Dermatol venereol, Dermatology, Dermatology morgan, Erythema, Erythema nodosum, Erythrocyte sedimentation rate, International journal, International society, Livedo, Livedo reticularis, Lower extremities, Mild cases, Myalgia, Ndings, Nodosa, Nodule, Periarteritis, Periarteritis nodosa, Polyarteritis, Polyarteritis nodosa, Reticularis, Review cutaneous polyarteritis nodosa, Rheum, Skin ulcers, Subcutaneous, Subcutaneous nodules, Subcutaneous tissue, Systemic, Systemic polyarteritis nodosa, Tender subcutaneous nodules, Ulceration, Urticarial vasculitis, Vasculitis.
Abstract
Cutaneous polyarteritis nodosa is a rare form of vasculitis relating to small‐to‐medium‐sized arteries. Its etiology is unknown. Clinical manifestations include tender subcutaneous nodules, livedo reticularis, cutaneous ulcers and necrosis. Although it is distinct from systemic polyarteritris nodosa in that it lacks significant internal organ involvement, extra‐cutaneous manifestations may be evident. Commonly encountered symptoms include fever, malaise, myalgias, arthralgias, and paresthesias. Exclusion of systemic polyarteritis nodosa is essential in diagnosis. The clinical course is chronic with remissions, relapses, and a favorable prognosis. Mild cases may resolve with nonsteroidal anti‐inflammatory drugs. If more severe, treatment with systemic corticosteroids generally achieves adequate response; however, adjunctive therapy is often necessary to allow reduction in steroid dosage.
Url:
DOI: 10.1111/j.1365-4632.2010.04522.x
Affiliations:
Links toward previous steps (curation, corpus...)
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Le document en format XML
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<front><div type="abstract" xml:lang="en">Cutaneous polyarteritis nodosa is a rare form of vasculitis relating to small‐to‐medium‐sized arteries. Its etiology is unknown. Clinical manifestations include tender subcutaneous nodules, livedo reticularis, cutaneous ulcers and necrosis. Although it is distinct from systemic polyarteritris nodosa in that it lacks significant internal organ involvement, extra‐cutaneous manifestations may be evident. Commonly encountered symptoms include fever, malaise, myalgias, arthralgias, and paresthesias. Exclusion of systemic polyarteritis nodosa is essential in diagnosis. The clinical course is chronic with remissions, relapses, and a favorable prognosis. Mild cases may resolve with nonsteroidal anti‐inflammatory drugs. If more severe, treatment with systemic corticosteroids generally achieves adequate response; however, adjunctive therapy is often necessary to allow reduction in steroid dosage.</div>
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